Hypothalamic Neoplasms - Pathology
Research News and Information

Sunday, November 22, 2009

Bilateral gonadoblastoma with dysgerminoma and pilocytic astrocytoma with WT1 GT-IVS9 mutation: A 46 XY phenotypic female with Frasier syndrome.

13 Dec 2009 Frasier syndrome is characterized by a 46 XY disorder of sex development, nephropathy, and increased risk for gonadoblastoma due to Wilms tumor 1(WT1) mutation in the donor splice site of intron-9, resulting in the splice form +KTS. Germ cell tumors ... Read more...

Endoscopic disconnection of hypothalamic astrocytoma causing gelastic epilepsy. Case report.

30 Jul 2009 The authors report on a case of juvenile pilocytic astrocytoma (JPA) and concomitant hypothalamic hamartoma (HH) with gelastic epilepsy that was successfully treated with endoscopic disconnection. This 6-year-old girl presented with prolonged, ... Read more...

Hypothalamic lipoma associated with severe obesity. Report of 2 cases.

30 Jul 2009 The association between hypothalamic dysfunction and obesity is well documented in both clinical and experimental models. The authors describe 2 children who developed obesity that could not be explained by endocrinological, genetic, or eating ... Read more...

Latest indexed articles for 'Hypothalamic Neoplasms - Pathology'

These are the very latest articles for this heading:

• Bilateral gonadoblastoma with dysgerminoma and pilocytic astrocytoma with WT1 GT-IVS9 mutation: A 46 XY phenotypic female with Frasier syndrome. 13 Dec 2009
• Endoscopic disconnection of hypothalamic astrocytoma causing gelastic epilepsy. Case report. 30 Jul 2009
• Hypothalamic lipoma associated with severe obesity. Report of 2 cases. 30 Jul 2009
• [Clinical and imaging features of hypothalamic hamartoma in children] 29 Apr 2009
• Tumor stabilization under treatment with imatinib in progressive hypothalamic-chiasmatic glioma. 30 Mar 2009
• Chemotherapy with cisplatin and vincristine for optic pathway/hypothalamic astrocytoma in young children. 15 Feb 2009
• Mixed germ cell tumor of the pituitary-hypothalamic region presenting as craniopharyngioma: case report and review of the literature. 29 Nov 2008
• Suprasellar hemangioblastoma. 29 Nov 2008
• Hypothalamic papillary tumor in a patient with tuberous sclerosis. 29 Sep 2008
• Loss of myelinated retinal nerve fibers from chronic papilledema. 30 Aug 2008
• Clinicopathological features and global genomic copy number alterations of pilomyxoid astrocytoma in the hypothalamus/optic pathway: comparative analysis with pilocytic astrocytoma using array-based comparative genomic hybridization. 9 Jul 2008
• Role of surgery for optic pathway/hypothalamic astrocytomas in children. 6 Jul 2008
• Endoscopic resection of hypothalamic hamartomas for refractory symptomatic epilepsy. 20 Apr 2008
• Ectopic hyperprolactinaemia in a woman with a mesocolic perivascular epithelioid cell tumor ("PEComa"). 16 Apr 2008
• Transtemporal-transchoroidal approach and its transamygdala extension to the posterior chiasmatic cistern and diencephalo-mesencephalic lesions. Mar 2008
• An unusual association of a sellar gangliocytoma with a prolactinoma. 30 Dec 2007
• Intractable gelastic seizures during infancy: ictal positron emission tomography (PET) demonstrating epileptiform activity within the hypothalamic hamartoma. 24 Dec 2007
• Gelastic seizures misdiagnosed as gastroesophageal reflux disease. 29 Apr 2007
• Hypothalamic hamartoma with bilateral anophthalmia. 18 Apr 2007
• [Gelastic seizures and low-grade hypothalamic astrocytoma] 30 Aug 2006

See a longer list of these articles.

Technical information about 'Hypothalamic Neoplasms'

Definition: Benign and malignant tumors of the HYPOTHALAMUS. Pilocytic astrocytomas and hamartomas are relatively frequent histologic types. Neoplasms of the hypothalamus frequently originate from adjacent structures, including the OPTIC CHIASM, optic nerve (see OPTIC NERVE NEOPLASMS), and pituitary gland (see PITUITARY NEOPLASMS). Relatively frequent clinical manifestations include visual loss, developmental delay, macrocephaly, and precocious puberty. (From Devita et al., Cancer: Principles and Practice of Oncology, 5th ed, p2051)

Descriptor UI: D007029

Alternative terms: Hypothalamic Neoplasms; Hypothalamus Neoplasms; Hypothalamus Neoplasm; Neoplasm, Hypothalamus; Tumors, Hypothalamus; Hypothalamus Tumor; Hypothalamus Tumors; Tumor, Hypothalamus; Neoplasms, Hypothalamus; Hypothalamic Tumors; Hypothalamic Tumor; Tumor, Hypothalamic; Tumors, Hypothalamic; Neoplasms, Hypothalamic; Hypothalamic Neoplasm; Neoplasm, Hypothalamic; Hypothalamic Cancer; Cancer, Hypothalamic; Cancers, Hypothalamic; Hypothalamic Cancers; Hypothalamic Neoplasms, Malignant; Hypothalamic Neoplasm, Malignant; Malignant Hypothalamic Neoplasm; Neoplasm, Malignant Hypothalamic; Neoplasms, Malignant Hypothalamic; Malignant Hypothalamic Neoplasms; Neoplasms, Hypothalamic, Malignant; Hypothalamic-Pituitary Neoplasms; Hypothalamic Pituitary Neoplasms; Hypothalamic-Pituitary Neoplasm; Neoplasm, Hypothalamic-Pituitary; Neoplasms, Hypothalamo-Neurohypophysial Region; Neoplasms, Hypothalamo Neurohypophysial Region; Hypothalamo-Neurohypophysial Region Neoplasms; Hypothalamo Neurohypophysial Region Neoplasms; Hypothalamo-Neurohypophysial Region Neoplasm; Neoplasm, Hypothalamo-Neurohypophysial Region; Neoplasms, Hypothalamic-Pituitary; Neoplasms, Hypothalamic Pituitary; Hypothalamic Teratomas; Hypothalamic Teratoma; Teratoma, Hypothalamic; Teratomas, Hypothalamic; Hypothalamic-Chiasmatic Neoplasms; Hypothalamic Chiasmatic Neoplasms; Hypothalamic-Chiasmatic Neoplasm; Neoplasm, Hypothalamic-Chiasmatic; Neoplasms, Hypothalamic-Chiasmatic; Neoplasms, Hypothalamic Chiasmatic; Benign Hypothalamic Neoplasms; Benign Hypothalamic Neoplasm; Neoplasm, Benign Hypothalamic; Neoplasms, Hypothalamic, Benign; Hypothalamic Neoplasms, Benign;

Allowable Qualifiers: blood; blood supply; cerebrospinal fluid; chemically induced; classification; complications; congenital; diagnosis; diet therapy; drug therapy; economics; embryology; enzymology; ethnology; etiology; genetics; history; immunology; metabolism; microbiology; mortality; nursing; epidemiology; parasitology; pathology; physiopathology; prevention & control; psychology; radiography; radionuclide imaging; radiotherapy; rehabilitation; secondary; secretion; surgery; therapy; ultrastructure; urine; veterinary; ultrasonography; chemistry; virology;

Tree Number: C04.588.614.250.195.885.500; C10.228.140.211.885.500; C10.228.140.617.477; C10.551.240.250.700.500;

History Note: 1981

Technical Notes: coord IM with site in hypothalamus (IM) + histol type of neopl (IM)