Wegener's granulomatosis: a new entity in the growing differential diagnosis of Degos' disease.

Full Abstract

Wegener's granulomatosis (WG) is a multisystemic vasculitis, with skin involvement in 14% of cases and with palpable purpura, subcutaneous nodules and necrotic papules as the common features.(1) We present a patient diagnosed with WG who had multiple whitish papules similar to those of malignant atrophic papulosis (Degos' disease), which appeared during a flare of his disease. Lesions of malignant atrophic papulosis are said to be pathognomonic; nevertheless, various diseases with similar clinical lesions have been described. To our knowledge, this is the first reported case of such lesions in a patient with WG, and we suggest WG should be included in the differential diagnosis of Degos' disease.

Author information

Author/s: Guhl, G (G); Diaz-Ley, B (B); Delgado, Y (Y); Daudén, E (E); Fraga, J (J); García-Diez, A (A);

Affiliation: Dermatology Services, Hospital Universitario de la Princesa, Madrid, Spain. guhl(-atsign-)aedv.es

Journal and publication information

Publication Type: Case Reports; Journal Article

Journal: Clinical and experimental dermatology (Clin Exp Dermatol), published in England. (Language: eng)

Reference: 2009-Jul; vol 34 (issue 5) : pp e1-3

Dates: Created 2009/06/10; Completed 2009/07/27;

PMID: 19040518, status: MEDLINE (last retrieval date: 8/20/2009, IMS Date: )

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